Angiosarcoma

Dr Shu Su and Dr Donna D'Souza et al.

 Angiosarcomas (like hemangiopericytomas and haemangioendotheliomas) are tumors that arise from vascular structures. They are typically difficult to distinguish from one another on imaging alone.

Angiosarcomas, are the most aggressive of the three, frequently having metastases at the time of diagnosis (and therefore carrying an extremely poor prognosis), and often having local recurrences. 

Epidemiology

They account for less than 1% of all sarcomas and are more frequently seen in males (M:F = 2:1) except when seen in the setting of post-mastectomy lymphoedema which is clearly more common in women and is known as Stewart-Treves syndrome.

Pathology

The malignant cells express morphological and functional properties of endothelial cells. The tumors can be multicentric with hemorrhage and necrosis being common.

Location specific lesions
Associations
Share article

Article information

rID: 900
System: Vascular
Tag: cases
Synonyms or Alternate Spellings:
  • Angiosarcoma (General)

Support Radiopaedia and see fewer ads

Cases and figures

  • Case 1: pulmonary angiosarcoma
    Drag here to reorder.
  • Updating… Please wait.

     Unable to process the form. Check for errors and try again.

     Thank you for updating your details.