Bat wing 4th ventricle sign refers to the morphology of the fourth ventricle in the Joubert anomaly and related syndromes. The absence of a vermis with apposed cerebellar hemispheres give the fourth ventricle an appearance reminiscent of a bat with its wings outstretched.
It is best demonstrated on an axial imaging plane and could be easily missed on sagittal and coronal images 3.
- 1. Barkovich AJ. Pediatric Neuroimaging (Pediatric Neuroimaging (Barkovich)). Lippincott Williams & Wilkins. ISBN:0781757665. Read it at Google Books - Find it at Amazon
- 2. Van beek EJ, Majoie CB. Case 25: Joubert syndrome. Radiology. 2000;216 (2): 379-82. Radiology (citation) - Pubmed citation
- 3. Sattam SL. Nahla A A.Yasser RF. Joubert syndrome: accuracy of neuro-radiological indings. Journal of Pediatric Neurology, Vol. 2, No. 1, 2004, pp. 33-37