Lasjaunias classification of vein of Galen aneurysmal malformations
The Lasjaunias classification, at the time of writing (mid 2016), is one of the two commonly used systems for classifying vein of Galen malformations. It relies on dividing the entity into choroidal or mural types, depending on the number and origin of feeding arteries.
- multiple feeders including thalamoperforating, choroidal and pericallosal arteries are located in the subarachnoid space in the choroidal fissure
- converge on a fistula site at the anterior aspect of the median prosencephalic vein (MPV)
- tend to present earlier (neonate) with more severe shunts
- this type of VGAM results in high output cardiac failure because of multiple high flow fistulas with less outflow restriction
- fistulae in the subarachnoid space in the wall of the median prosencephalic vein
- supply may be unilateral or bilateral
- associated with absence or stenosis of dural sinuses
- associated with stenosis at the level of the jugular foramen
- present later (infant) and typically with hydrocephalus
- this type of VGAM presents with fewer fistulas with high outflow restriction
- 1. Jones Blaise V., William S. Ball, Thomas A. Tomsick et al. “Vein of Galen Aneurysmal Malformation: Diagnosis and Treatment of 13 Children with Extended Clinical Follow-up.” AJNR Am J Neuroradiol 23, no. 10 (November 1, 2002): 1717-1724. [Link].
- 2. Lasjaunias Pierre L. Vascular diseases in neonates, infants and children. Springer, 1997. ISBN: 3540608451, 9783540608455.
- 3. Albright AL, Pollack IF. Principles and Practice of Pediatric Neurosurgery. Thieme. (2011) ISBN:1604064609. Read it at Google Books - Find it at Amazon